Aucte intermittent porphyria and epilepsy.

نویسندگان

  • R Biagini
  • R Tignani
  • A R Fifi
  • L Nappini
چکیده

A 14-year-old boy had suffered from intermittent acute hepatic porphyria, myoclonic convulsions and mental retardation (Lennox-Gastaut syndrome). The porphyria was treated by stopping the administration of phenobarbitone and phenytoin. Sodium valproate at a dose of 70 mg/kg per day lessened the severity and frequency of convulsive crises.

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عنوان ژورنال:
  • Archives of disease in childhood

دوره 54 8  شماره 

صفحات  -

تاریخ انتشار 1979